Introduction. Pierre Robin Sequence (PRS) is a congenital abnormality associated with the first brachial arch malformation. The etiology of PRS is not fully known, though both genetic and environmental factors are taken into account. PRS symptoms (micrognathia, glossoptosis and cleft palate) have a significant influence on the proper development of a child. The severity of the disease determines the treatment plan and its results. Aim. The aim of this report is to present the case of a five-year old boy diagnosed with PRS. Material and methods. A clinical examination of the oral cavity was performed, an orthopantomogram was taken. Results. Visible changes in facial features, bird face appearance, scar after surgical reconstruction of soft palate, dental caries. Conclusions. The course of treatment

Key words: Pierre‑Robin Sequence, cleft palate, micrognathia.