Ectodermal dysplasia is the term used to describe a large and heterogenic group of congenital disorders. Ectodermal dysplasia affects at least two ectoderm-derived structures. The dental abnormalities associated with ectodermal dysplasia are hipodontia, oligodontia and even anodontia. Aim of the study. The authors describe a clinical case of 5-year-old boy with hereditary hidrotic ectodermal dysplasia. Materials and methods. The first stage in the clinical treatment of a young patient affected by ectodermal dysplasia is presented. Complete dentures were made. Conclusion. Early prosthetic rehabilitation of juvenile patients with ectodermal dysplasia is a very complex problem. Early rehabilitation and an interdisciplinary approach are essential for successful treatment.

Key words: Ectodermal Dysplasia, hipodontia, anodontia, early prosthetic treatment.