A case report literature review was performed regarding orthodontic treatment of malocclusions and dental defects in children with cleidocranial dysplasia (CCD). Articles describing orthodontic treatment were analyzed and the own case report was presented. Malocclusion correction in majority of cases involved both orthodontic and surgical treatment. The treatment strategy performed by the authors included the removal of persistent primary teeth and majority of supernumerary teeth, surgical exposure of impacted permanent teeth, followed by orthodontic treatment. Only one study presented the outcome of comprehensive, long-term, orthodontic-surgical-prosthetic therapy in two patients with CCD. In the presented own case of CCD patient, orthodontic treatment was completed.

Key words: cleidocranial dysplasia, orthodontic therapy, dental and occlusal disorders.